Pleuropulmonary blastoma (
PPB) is a rare
cancer originating in the
lung or
pleural cavity. It occurs most often in infants and young children but also has been reported in adults. In a retrospective review of 204 children with lung tumors, pleuropulmonary blastoma and
carcinoid tumor were the most common primary tumors (83% of the 204 children had secondary tumors
spread from cancers elsewhere in the body). Pleuropulmonary blastoma is regarded as
malignant.